Abstract:ObjectiveTo explore the clinical and diagnostic features of hemiconvulsion-hemiplegia-epilpsy syndrome(HHES). MethodsThe clinical data of one case with HHES admitted to the Pediatrics Department of HeBei General Hospital on April 16, 2018 were retrospectively analyzed, and relevant literatures were reviewed. ResultsThe child began with convulsion of the right limb, and later presented as convulsion persistent state, hemiplegia of the left limb, and repeated convulsion after improvement. Cranial CT and cranial magnetic resonance imaging (MRI) indicated calcification. The video electroencephalogram (VEEG) showed the rhythm of continuous spines and slow spines at low and middle amplitude in the right occipital region in seizure period. The VEEG reexamination after the improvement of the child in intermittent period showed a large amount of diffuse slow wave activity with a medium to high amplitude of 1.5-3.0Hz were observed in each lead in both hemispheres, with the left hemisphere significantly more than the right hemisphere. Seizure period: no epilepsy was observed in monitoring. ConclusionIn children with HHES, electroencephalography and characteristic neuroimaging abnormalities are helpful for the diagnosis of HHES.
王灵君 娄燕. 偏侧惊厥-偏瘫-癫痫综合征的诊断学特征并文献复习[J]. 中华诊断学电子杂志, 2020, 8(2): 126-129.
Wang Lingjun,Lou Yan. Diagnostic features of hemiconvulsionhemiplegiaepilpsy syndrome and literature review. zhzdx, 2020, 8(2): 126-129.